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Synonyms: N-Carbamyl-L-glutamic acid
Carglumic acid (N-Carbamyl-L-glutamic acid), a functional analogue of N-acetylglutamate (NAG) and a carbamoyl phosphate synthetase 1 (CPS1) activator, is used to treat acute and chronic hyperammonemia associated with NAG synthase (NAGS) deficiency.
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18817579266
实验数据
技术信息
CAS号 | 1188-38-1 | 储存条件 |
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分子式 | C6H10N2O5 | 运输 | 蓝冰 | |||
分子量 | 190.15 | 别名 | N-Carbamyl-L-glutamic acid | |||
溶解度 |
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动物实验配方 |
生物活性